X-Linked Stapes Gusher: CT Findings in One Patient

Summary: A 31-year-old male patient presented with progressive mixed hearing loss since birth. A stapedectomy was attempted and was unsuccessful because of perilymph gushing. CT of the temporal bones showed bulbous dilatation of the fundi of the internal auditory canals and absence of the bone plates separating them from the base of the cochleas. This unusual abnormality was found after the attempted stapedectomy and explains the clinical findings. The findings in male patients are fairly typical X-linked congenital deafness.

Congenital X-linked Stapes Gusher Syndrome in an Infant

PDF) X-linked stapes gusher: CT findings in one patient

A Case Series of X-Linked Deafness-2 with Sensorineural Hearing Loss, Stapes Fixation, and Perilymphatic Gusher: MR Imaging and Clinical Features of Hypothalamic Malformations

X-linked deafness, Radiology Case

Axial 3D T2WI in a male patient with X-linked deafness with mixed

Computed tomography image of the temporal bone of a patient with HDR

Enlarged Cochlear Aperture as a Risk Factor for Cerebrospinal Fluid Gusher During Cochlear Implant Surgery - Kevin Wong, Zachary G. Schwam, Vivian Z. Kaul, George B. Wanna, 2022

Cabinet Messidor, Bruxelles Uccle Tympanoplasty - Gusher as a complication in otosclerosis surgery : how to prevent and react - Cabinet Messidor, Bruxelles Uccle

Congenital Temporal Bone Anomalies: An Embryologic Approach - ppt video online download

Internal auditory canal meningocele‐perilabyrinthine/translabyrinthine fistula: Case report and imaging - Truesdale - 2016 - The Laryngoscope - Wiley Online Library

Spectrum of Third Window Abnormalities: Semicircular Canal Dehiscence and Beyond. - Abstract - Europe PMC

Gusher in Stapedotomy - A Case Report

Imaging of inner ear malformations: a primer for radiologists